Neonatal cholestasis with ductal paucity and steatosis.

History: A 3.5-months-old male presented to us with small bowel type of diarrhea and recurrent non-bilious vomiting since birth; jaundice since 2.5 months of age; swelling all over body, clay colored stools, fever, cough and respiratory difficulty since 3 months of age, and refusal to feed from 2 days prior to admission. He also had prolonged bleeding at the site of intramuscular injection. There was no history of abnormal movements or altered sensorium. Investigations previously done at another center revealed severe anemia (Hb 5.7 g/dL), coagulopathy (prothrombin time 1 min) and lower respiratory tract infection, for which he had received three units of whole blood transfusion, vitamin K and parenteral antibiotics, and subsequently referred to our center.